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J99 Billable Code

Respiratory disorders in diseases classified elsewhere

Effective From: 10/01/2016

Chapter Classification

Chapter 10 Diseases of the respiratory system (J00-J99)

Section Detail

J96-J99 Other diseases of the respiratory system (J96-J99)

Coding Guidelines & Notes

codeFirst
  • underlying disease, such as:
  • amyloidosis (E85.-)
  • ankylosing spondylitis (M45.-)
  • congenital syphilis (A50.-)
  • cryoglobulinemia (D89.1)
  • early congenital syphilis (A50.0-)
  • plasminogen deficiency (E88.02)
  • schistosomiasis (B65.0-B65.9)
excludes1
  • respiratory disorders in:
  • amebiasis (A06.5)
  • blastomycosis (B40.0-B40.2)
  • candidiasis (B37.1)
  • coccidioidomycosis (B38.0-B38.2)
  • cystic fibrosis with pulmonary manifestations (E84.0)
  • dermatomyositis (M33.01, M33.11)
  • histoplasmosis (B39.0-B39.2)
  • late syphilis (A52.72, A52.73)
  • polymyositis (M33.21)
  • Sjögren syndrome (M35.02)
  • systemic lupus erythematosus (M32.13)
  • systemic sclerosis (M34.81)
  • Wegener's granulomatosis (M31.30-M31.31)

OPPS Editing Flags

External Cause No
Mental Health No
Manifestation (Edit 89) Yes
Code First Applicable ?This code represents a manifestation of an underlying disease. The underlying condition must be coded first as the principal diagnosis. No
Unacceptable PDX (Edit 113) No

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